RT Book, Section A1 Rothenberg, Steven A1 Crombleholme, Timothy M. A2 Ziegler, Moritz M. A2 Azizkhan, Richard G. A2 Allmen, Daniel von A2 Weber, Thomas R. SR Print(0) ID 1100433516 T1 Congenital Lung Malformations: CPAM, Bronchopulmonary Sequestration, Congenital Lobar Emphysema, and Bronchogenic Cyst T2 Operative Pediatric Surgery, 2e YR 2014 FD 2014 PB McGraw-Hill Education PP New York, NY SN 978-0-07-162723-8 LK accesspediatrics.mhmedical.com/content.aspx?aid=1100433516 RD 2024/10/12 AB Treatment of bronchopulmonary malformations may vary somewhat depending on the time of diagnosis and the presentation, but in most cases, complete resection is the desired therapy.New minimally invasive techniques allow treatment with much less pain and morbidity and long-term consequence for the infant or child.Bronchopulmonary sequestration (BPS) lesions may be asymptomatic, but postnatal resection should be considered because of the risks of infection, hemorrhage, and malignant transformation.The surgical approach to BPS is straightforward, with the exception of the management of anomalous blood supply. Intraoperative death due to hemorrhage from unrecognized anomalous vessels has been reported.Congenital pulmonary airway malformation (CPAM) is increasingly being diagnosed by routine prenatal ultrasound, allowing for prenatal consultation and planning. The need for fetal intervention is rare and limited to cases with severe hydrops and a predicted mortality of near 100%.The treatment of choice in infants with CPAM is complete resection of the CPAM, usually by lobectomy.The treatment for patients with symptomatic congenital lobar emphysema (CLE) is surgical resection; in most cases, a complete lobectomy.The operative approach to resecting bronchogenic cysts depends on their location and involvement of adjacent structures, such as the trachea or mainstem bronchi, which may require repair.