RT Book, Section A1 Eng, Katharine A1 Alkhouri, Naim A2 Usatine, Richard P. A2 Sabella, Camille A2 Smith, Mindy Ann A2 Mayeaux, E.J. A2 Chumley, Heidi S. A2 Appachi, Elumalai SR Print(0) ID 1114872397 T1 Neonatal Cholestasis T2 The Color Atlas of Pediatrics YR 2015 FD 2015 PB McGraw-Hill Education PP New York, NY SN 978-0-07-176701-9 LK accesspediatrics.mhmedical.com/content.aspx?aid=1114872397 RD 2024/04/20 AB A 4-week-old full-term female is seen for routine follow-up with her pediatrician. Her mother reports that she has been taking breast milk well with good weight gain. She has no specific concerns; however does report she noticed lighter colored stools recently. On physical exam, jaundice and scleral icterus are noted, along with dark urine in her diaper. The pediatrician orders labs drawn urgently and calls the pediatric gastroenterologist for immediate assistance. The work-up is expedited and she is found to have biliary atresia (Figures 61-1 and 61-2). The Kasai portoenterostomy procedure is performed to treat the cholestatic jaundice. This surgery involves exposing the porta hepatis and attaching part of the small intestine to the exposed liver surface to allow bile to drain out of the liver into the intestines.